Hereditary angioedema: a rare but potentially lethal disease.
نویسندگان
چکیده
Hereditary angioedema, although uncommon, should be considered in the differential diagnosis of all patients with facial edema. In this article, we present a case of hereditary angioedema and discuss the presentation, diagnosis, and management of the disease.
منابع مشابه
Report on the First Survey of Iranian Patients with Hereditary Angioedema
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Hereditary angioedema is a rare disorder of complement system which is often seen with autosomal dominant hereditary. Clinical characteristics include non- pruritic and non-pitting mucocutaneous edema that could involve all parts of the body. This study reports seven cases of hereditary angioedema with classical manifestations accompanied by low function of C1INH (type 2). One death occurred du...
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عنوان ژورنال:
- The Journal of the Louisiana State Medical Society : official organ of the Louisiana State Medical Society
دوره 154 3 شماره
صفحات -
تاریخ انتشار 2002